Current management of the feminizing genitoplasty in congenital adrenal hyperplasia with low vaginal confluence
Hanae Khir Allah, Aya Skiredj, Meryam Ramzi, Mohamed Amine Bouhafs
Purpose: Highlighting the importance of evolution of techniques of feminizing genitoplasty in congenital adrenal hyperplasia(CAH) with low vaginal confluence. introduction: Surgical aims for virilized girls with CAH are to create cosmetic and functional external genitalia from a sexual, reproductive and urinary standpoint. observation: Patient aged 1 year and 7 months, without specific antecedents, followed for CAH, with karyotype 46, XX, and signs of virilization stage III of Prader. the patient benefited from the posterior based omega-shaped flap vaginoplasty and the clitoroplasty technique of subtunical excision of erectile tissue with preservation of the neurovascular bundle. Conclusion : Surgical technique for virilized genitalia in CAH has evolved from excisional surgery of the clitoris, to very refined surgery with precise anatomical land- marks to preserve the majority of nerve terminals in reductions clitoroplasty. Several aspects of vaginoplasty and introitoplasty had been developed to improve cosmetic appearance.
Hanae Khir Allah, Aya Skiredj, Meryam Ramzi, Mohamed Amine Bouhafs. Current management of the feminizing genitoplasty in congenital adrenal hyperplasia with low vaginal confluence. International Journal of Medicine Research, Volume 4, Issue 1, 2019, Pages 69-73