Vol. 4, Issue 1 (2019)
Current management of the feminizing genitoplasty in congenital adrenal hyperplasia with low vaginal confluence
Author(s): Hanae Khir Allah, Aya Skiredj, Meryam Ramzi, Mohamed Amine Bouhafs
Abstract: Purpose: Highlighting the importance of evolution of techniques of feminizing genitoplasty in congenital adrenal hyperplasia(CAH) with low vaginal confluence. introduction: Surgical aims for virilized girls with CAH are to create cosmetic and functional external genitalia from a sexual, reproductive and urinary standpoint. observation: Patient aged 1 year and 7 months, without specific antecedents, followed for CAH, with karyotype 46, XX, and signs of virilization stage III of Prader. the patient benefited from the posterior based omega-shaped flap vaginoplasty and the clitoroplasty technique of subtunical excision of erectile tissue with preservation of the neurovascular bundle. Conclusion : Surgical technique for virilized genitalia in CAH has evolved from excisional surgery of the clitoris, to very refined surgery with precise anatomical land- marks to preserve the majority of nerve terminals in reductions clitoroplasty. Several aspects of vaginoplasty and introitoplasty had been developed to improve cosmetic appearance.
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